Multiple Endocrine Neoplasia Type 1 Initially Presenting as Extensive Bone Metastases from Pancreatic Neuroendocrine Tumor: A Case Report
Multiple endocrine neoplasia type 1 (MEN1) is a hereditary tumor syndrome classically involving the parathyroid glands, pancreatic neuroendocrine tumors (pNETs), and pituitary adenomas. pNETs in MEN1 usually present with hormonal symptoms or liver metastasis, while bone metastasis as the dominant initial presentation...