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Longitudinal Characterization of the Microbiological Status in Primary Ciliary Dyskinesia: An Italian Multicentre Study

V. Ferraro Valentina Tonazzo A. Pandolfo Claudia Biondi Alessandra Boni Melissa Borrelli C. Calogero Alberta Circiello A. Corcione R. Cutrera Valentina Fainardi G. Parisi M. F. Patria G. Scopelliti N. Ullmann Silvia Carraro
Oct 2026 · Pediatric Pulmonology · Vol 61 · 0 citations · 24 references
Medicine

TL;DR

Prevalence and longitudinal changes of respiratory microbiological profile in children and young adults with PCD, and their association with clinical, functional, and radiological features are evaluated.

Abstract

Primary Ciliary Dyskinesia (PCD) is a genetic disorder characterized by respiratory infections leading to chronic airway colonization and progressive lung damage. The aim of this study is to evaluate prevalence and longitudinal changes of respiratory microbiological profile in children and young adults with PCD, and their association with clinical, functional, and radiological features.

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